ABSTRACT

Ewing sarcoma/ PNET of the orbit is usually a metastatic tumor. Primary orbital Ewing sarcoma/ PNET is extremely rare with only 17 reported cases as per literature. One such rare case of a primary extraskeletal Ewing sarcoma/PNET of the orbit, which is anĀ  extraordinary site for its occurrence in a 4year old boy, is presented here.